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2019

Copyright (c) 2019 Carlos Arturo Paniagua-Coahuila, Crescencio Martínez-Martínez , José Luis Arellano-Hernández , Dulce Alejandra Alonso-Lozano , Freddy Mendoza-Hernández , Hugo Mendieta Zerón

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Klippel Trenaunay Weber syndrome in pregnancy. Case report and literature review

https://doi.org/10.17081/innosa.75
Carlos Arturo Paniagua-Coahuila
Hospital Materno Perinatal Mónica Pretelini Sáenz, Toluca, México.
https://orcid.org/0000-0002-4551-0923
Crescencio Martínez-Martínez
Hospital Materno Infantil Instituto de Seguridad Social del Estado de México y Municipios, Toluca, México
https://orcid.org/0000-0001-8976-9630
José Luis Arellano-Hernández
Hospital Materno Infantil Instituto de Seguridad Social del Estado de México y Municipios, Toluca, México
https://orcid.org/0000-0003-2676-1302
Dulce Alejandra Alonso-Lozano
Hospital Materno Infantil Instituto de Seguridad Social del Estado de México y Municipios, Toluca, México
https://orcid.org/0000-0003-2023-0498
Freddy Mendoza-Hernández
Hospital Materno Infantil Instituto de Seguridad Social del Estado de México y Municipios, Toluca, México
Hugo Mendieta Zerón
Hospital Materno Perinatal Mónica Pretelini Sáenz, Toluca, México
https://orcid.org/0000-0003-3492-8950

Corresponding Author(s) : Carlos Arturo Paniagua-Coahuila

dr.carlosarturopaniagua@gmail.com

Ciencia e Innovación en Salud, 2019

Abstract

Background: Klippel-Trenaunay syndrome (SKT) is a congenital disorder characterized by the presence of vascular cutaneous nevus, venous malformations, and soft tissue and bone hypertrophy affecting one or more extremities.


Case report: A 20-year-old female, primiparous, diagnosed with SKT since childhood, was attended at 34 weeks of gestation with multiple cervical and vulvar varices and the presence of a vasculocutaneous nevus in the right pelvic limb; Contrast angioresonance was performed, where multiple arteriovenous malformations were confirmed at the level of the right pelvic limb, compromising the inguinal, vulvar, femoral region and discreetly the uterine segment. Treatment with low molecular weight heparin was started until it was suspended 24 hours prior to the scheduling of caesarean section at 39.1 weeks of gestation.


Discussion: An uncomplicated newborn was obtained with transsurgical bleeding of 450 ml. She went home 48 hours post-surgery without evidence of complications and subsequent follow-up in an outpatient clinic for angiology and obstetric critical medicine.

Keywords

Klippel-Trenaunay syndrome, pregnancy, evolution
1.
Paniagua-Coahuila CA, Martínez-Martínez C, Arellano-Hernández JL, Alonso-Lozano DA, Mendoza-Hernández F, Mendieta Zerón H. Klippel Trenaunay Weber syndrome in pregnancy. Case report and literature review. Ciencia e Innovación en Salud [Internet]. 2019 Nov. 23 [cited 2024 Apr. 18];6. Available from: https://revistas.unisimon.edu.co/index.php/innovacionsalud/article/view/4190
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